Publications by authors named "Joseph H Nogajski"
Congenital myasthenic syndromes (CMS) are a heterogeneous group of uncommon, inherited disorders affecting the neuromuscular junction. The defects interfere with presynaptic, synaptic, or postsynaptic function and compromise neuromuscular transmission. Most patients with CMS have similar clinical features regardless of the underlying defect, but attention to clinical and electrodiagnostic parameters can narrow the diagnostic spectrum.
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- The study investigated two tests, VEMPs and OVEMPs, to assess the vestibular system and identify lesions in the brainstem.
- Results showed delayed responses in the left side for both types of tests, indicating a possible issue related to demyelination.
- The findings suggest that these tests can help localize and understand the characteristics of vestibular pathway lesions.
The present study was undertaken to quantitate the incidence and clinical patterns of peripheral nerve dysfunction distal to the level of injury in patients with spinal cord injury (SCI). Through retrospective analysis, SCI patients were identified after referral for neurophysiologic investigation of new neuropathic symptoms. In total, peripheral nerve or nerve root lesions developed in 34 SCI patients, most commonly within the first year after SCI.
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