Hepatic Vascular Disorders: From Diagnosis to Interventional Radiology.

Hepatic vascular pathology comprises a spectrum of diseases with specific imaging features that have portal hypertension as a common denominator. The imaging features of the main pathologies are described, such as portal thrombosis, Budd-Chiari syndrome, hereditary hemorrhagic telangiectasia, portosystemic shunts and congenital vascular malformations. Endovascular intervention techniques are listed according to the indication for each hepatic vascular pathology and emphasis is placed on the ability to shape disease progression in order to prevent related morbidity and mortality.

Multistage closure of a congenital extrahepatic portosystemic shunt.

Background: Congenital extrahepatic portosystemic shunts (CEPS) are rare shunts connecting the extrahepatic portal system with the inferior vena cava. Shunt dimensions and the risk of portal hypertension determines the closure strategy. Endovascular treatment is indicated for single stage occlusion of longer length shunts, whereas the remaining shunt types are preferentially surgically occluded.

Congenital extrahepatic portosystemic shunt type II occluded with cardiac closure device.

Congenital extrahepatic portosystemic shunts are a rare cause of lower gastrointestinal bleeding in children. They result from the connection of a systemic vessel with the portomesenteric vasculature before the division of the main portal vein. Herein, we report a case of a congenital extrahepatic portosystemic shunts type II in a 4-year-old male diagnosed by Doppler ultrasonography during the investigation of abdominal pain and recurrent hematochezia, later confirmed by computed tomography.