Abnormal function of /p.R957P mutant in congenital cataract.

Aim: To identify genetic defects in a Chinese family with congenital posterior polar cataracts and assess the pathogenicity.

Methods: A four-generation Chinese family affected with autosomal dominant congenital cataract was recruited. Nineteen individuals took part in this study including 5 affected and 14 unaffected individuals.

Design and Experimental Study of a Large Beam Waist Streak Tube in an ICF Experiment.

In order to realize in situ multi-frame framing, this paper designed and developed a large-waist framing converter tube. The size ratio between the waist and the object was about 1.16:1.

Secondary Amplifier Sampling Component Design of an X-ray Framing Detector Based on a Streak Tube.

The development of inertial confinement fusion (ICF) experiments necessitates the diagnostic instrument to have multiple frames with a high spatial and temporal resolution for the two-dimensional detection of the hot spot at the implosion end of the ICF. The existing sampling two-dimensional imaging technology in the world has superior performance; however, its subsequent development requires a streak tube with large lateral magnification. In this work, an electron beam separation device was designed and developed for the first time.

Experimental measurement of the meridian Petzval image plane of a streak tube.

For an electron-optical imaging system with wide beam focusing, the calculation of the field curvature can be performed only theoretically and requires the specific analytical expressions of the axial potential distribution in the streak tube and its corresponding derivatives, making the calculation cumbersome. Even when the electron trajectory is tracked using the numerical calculation method, the calculated results cannot be verified experimentally. A method for measuring the field curvature of the streak tube based on the spherical fluorescent screen is proposed for the first time, to the best of our knowledge.

[Optimization immobilizing activated carbon and bacteria by sodium alginate and its character of adsorption of Pb2+].

Through the immobilized biosorption of activated carbon and Paenibacillus polymyxa GA1 by sodium alginate, this paper take advantage of the orthogonal experiment to investigate the adsorption characteristics of sodium alginate. According to the research, the optimal preparation conditions were as following: the mass fraction of sodium alginate was 2.5%; the amount of carbon and bacteria was 1:20 and 1:2, respectively; under the preparation condition, the adsorption rate could reach to 93.