Partial splenectomy for portal hypertension in cystic fibrosis related liver disease.

Aims: To review the middle- and long-term effects of partial splenectomy (PS) on portal hypertension (PHT) and its complications in patients with cystic fibrosis (CF) related liver disease risky PHT.

Method: Over a 20 years period, 19 patients aged 7-23 years underwent partial PS for massive splenomegaly, hypersplenism, and/ or severe PHT.

Results: In all but three cases, PHT and hypersplenism have improved for long periods.