A rare case of granular cell tumor affecting the upper back in a child.

Granular cell tumors (GCT) are rare mesenchymal tumors belonging to Schwann cell lineage constituting 0.5% of all soft tissue neoplasms. They occur in skin, subcutaneous tissues, mucosal surfaces including within the deeper organs.

Clinicodemographic profile and outcomes of congenital diaphragmatic hernia with sac: experience of a paediatric referral centre.

Introduction: Congenital diaphragmatic hernia, in which viscera herniate into the thoracic cavity, is one of the common causes of onset of respiratory distress in neonates and children. Developmentally they may have a sac in rare cases.

Aim: To analyse the clinical profile and the outcome of congenital diaphragmatic hernia with a sac in neonates and children in a paediatric referral centre.

A case of arteriovenous malformation of the hand and its outcome.

Introduction And Importance: AVMs are rarest congenital anomalies constituting around 1% of pediatric population. Arteriovenous malformations originate at 4th to 10th weeks of intra uterine life due to persistence of primitive arteriovenous shunts. Though the exact prevalence is unknown, upper limb constitute around 10 % of all AVMs.

Congenital duodenojejunal junction obstruction; report of two rare cases.

Introduction And Importance: Congenital obstruction of duodenojejunal junction is a rare unexplored pathologic entity. Most of the cases reported so far are regarding extrinsic band or narrower attachment of ligament of Treitz, which will be presenting with vomiting in neonates and children without malrotation.

Case Presentation: Author is reporting here two rare cases of congenital intrinsic duodenojejunal junctional obstruction and their management in toddlers.

A case of ganglioneuromatosis in a child and its outcome.

Introduction: Ganglioneuromas (GNs) are hamartomatous tumors that originate in sympathetic ganglia and adrenal glands. Rarely, they might originate in enteric nervous system affecting its motility. Clinically they present with varying symptoms of pain abdomen, constipation and bleeding.

A rare case of anterior mid line neck cyst in a child.

Introduction: Mid line neck swellings are common in paediatric as well as in adults. They can be of three categories; inflammatory, neoplastic, and congenital.

Case Presentation: A child with history of a nodular swelling over the anterior midline neck, its unusual diagnosis and its management has been discussed here.

A decompressing abdominal mass and its outcome in a child-case report.

Introduction: Mesenteric cysts are benign tumours occurring in both adults as well as in children; can be single or multiple, unilocular or multilocular.

Importance: Pure chylous cysts as presenting as decompressing mass are rarely reported so far.

Case Presentation: a 2year old male child presenting with vague fullness of the abdomen and occasional vomiting since 7months of age, on imaging studies revealed it to be giant mesenteric cyst.

Testicular torsion; clinical diagnosis or imaging diagnosis?

Testicular torsion is the most common urosurgical emergency in infants, children, and young adolescents, resulting in irreversible ischemic injury within hours; hence demanding urgent surgical attention. It has a bimodal distribution with the highest incidence occurring after puberty, followed by the neonatal period peak. Though the imaging modalities are helpful in the diagnosis, nothing can supersede the clinical findings and judgment.

Bell clapper deformity in female?

Introduction: Indirect inguinal hernia is one of the most common congenital anomaly common in males, but not uncommon in females. In females, inguinal hernia mostly indirect, containing ovary presenting as a palpable labial mass is common, resulting in strangulation, torsion, and infertility if left untreated.

Importance: The bell clapper deformity (BCD) is an important anatomical risk factor for intra vaginal testicular torsion, its presence in females is hardly been speculated.

A rare case of jejunal atresia.

Introduction: Intestinal atresia more common in the small bowel, apart from large intestine. Jejunal atresia characterized by complete occlusion of the intestinal lumen, is a rare congenital anomaly occurring in 1 in 12,000 live births.

Importance: The jejunal atresia can be single or multiple occurring anywhere from the ligament of Treitz to the jejuno-ileal junction, requiring immediate surgical attention to prevent mortality and morbidity among these neonates.

An Unusual Case of Neonatal Perianal Lesion and Its Management.

Infantile hemangiomas (IHs) are common vascular tumors occurring in infants. The IHs have a characteristic natural course. Most of the uncomplicated IHs undergo spontaneous involution, with a small proportion of cases requiring intervention.

An unusual manifestation of a foreign body airway in a toddler.

Foreign body (FBA) in the airway is a common cause of sudden onset of respiratory distress in children. Prompt recognition and early intervention is required to minimize the potentially serious and sometimes fatal consequences.

Early neonatal lobectomy for ILE; is it feasible?

Introduction: Congenital lobar emphysema (CLE) also called congenital lobar overinflation and infantile lobar emphysema is a rare congenital anomaly of lung often presents in the neonatal period, with hyperinflation of one or more pulmonary lobes.

Importance: Author is reporting here an uneventfully done earliest ever neonatal lobectomy for ILE.

Congenital right diaphragmatic defects: Our institutional experience.

Background: The descriptive clinical study was conducted to analyse the clinical profile as well as the outcome of congenital right diaphragmatic defects among children including neonates in a tertiary care referral neonatal and paediatric centre in southern Karnataka, India.

Materials And Methods: This retrospective and prospective observational clinical study was conducted from January 2005 to August 2019, over a period of 14.7 years in a tertiary care referral neonatal and paediatric centre.

A rare case of chest wall reconstruction in a child.

Introduction: Ewing sarcoma/primitive neuroectodermal tumour (ES/PNET) is the most common malignant tumour of the chest wall in children and young adults. Chest wall defect left after complete resection of the involved ribs and chest wall defect requiring reconstruction, is surgically challenging for cosmetic as well as for functional purposes especially in growing children.

Importance: A rare but feasible and simple technique for a case of chest wall tumour reconstruction has been described here with its successful outcome with available composite muscular vascularised flap.

Persistent Left Superior Vena Cava: A Rare Association.

Persistent left superior vena cava (PLSVC) is the most frequent abnormality in the general population with the frequency of 0.1% to 0.5%.

A giant thoraco abdominal wall lipoma in a child.

Lipomas are benign mesenchymatous soft tissue tumours occurring mostly in the subcutaneous areas of the body. They are usually asymptomatic painless swellings, presenting with a large size in adults. Giant lipomas are rarely reported in adults as well as in children.

A Vague Gluteal Swelling in a Neonate: Challenges in Its Diagnosis and Management. Short Title-Sacroccoygeal Teratoma.

Sacro coccygeal teratoma (SCT) is the most common extra gonadal neoplasm in the pre sacral area occurring in neonatal period. They mostly occur in the midline with a female preponderance. They are usually attached to coccyx, They are believed to be arising from totipotent cells that originate from primitive knot (Hensen's node), hence are usually attached to coccyx.

A Terminal Colovesical Fistula in an Anorectal Malformation.

Anorectal malformations are relatively common anomalies encountered in pediatric surgical practice. They are usually recognized at birth with absent anal canal or failure to pass meconium and hence can lead to life threatening bowel obstruction without surgical intervention. We are reporting a rare case of non-syndromic, sporadic, terminal colovesical fistula associated with high anorectal malformation not associated with congenital pouch colon in a neonate.

Pedunculated Perianal Mass in a Neonate: A Rare Case Report.

Congenital perianal pedunculated masses are a rare occurrence in neonates. They are benign in nature and can be excised completely for definitive diagnosis. Here is a report of a rare case of pedunculated perianal mass occurring in a neonate managed successfully.

Giant Colonic Lithobezoar: A Rare Case Report.

Bezoar is defined as the accumulation of undigested foreign bodies or nutrients in the gastrointestinal tract. Lithobezoar, the accumulation of stones in the digestive tract, is commonly seen in the stomach. We report a case of giant colonic lithobezoar in a child.

Stridor in a child: It's diagnostic challenges.

Introduction: Foreign body aspiration (FBA) is an extremely serious life threatening condition in infants and children.

Case Report: We are reporting a case of multiple foreign bodies lodged in respiratory tract in an infant.

Discussion: FBA is the most common cause of accidental death among infants and toddlers.