Publications by authors named "Jane Rice"

Article Synopsis
  • This study analyzes the protein and amino acid (AA) content of various fruits, vegetables, and starchy roots to help manage dietary restrictions for individuals with amino acid-related inherited metabolic disorders (IMDs) and urea cycle disorders (UCDs).
  • Utilizing high-performance liquid chromatography (HPLC) and the Dumas method on 165 food samples, the research finds that dried fruits and legumes have the highest protein and AA levels, while fruits and cruciferous vegetables have the lowest.
  • The results aim to provide valuable information for clinical practice, improving diet quality and metabolic control for those affected by these disorders.
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Phenylketonuria (PKU) is an inherited disorder of protein metabolism. It is generally treated using dietary management with limited intake of phenylalanine (Phe). Partial breastfeeding (BF) is encouraged among mothers of infants with PKU, together with a Phe-free mixture of synthetic amino acids.

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A 9-year-old boy presented with a 2-day history of vomiting, ataxia and reduced consciousness. He had vomited intermittently in the two preceding months, without headaches, visual disturbance or early morning symptoms. He had autism spectrum disorder, and restricted eating since aged 2 years, eating only corn-crisps, Rich Tea biscuits and chips (French fries), and drinking Coca-Cola (containing 10% glucose; figure 1).

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