Nutritional rehabilitation increases the resting energy expenditure of malnourished children with severe cerebral palsy.

Aim: The aim of this study was to measure resting energy expenditure (REE) and energy intake in children with quadriplegic cerebral palsy (CP), to relate these to anthropometric measurements, and to determine the influence of nutritional rehabilitation on REE.

Methods: Fifty-six children (20 females, 36 males; age range 3y 11mo-18y; mean age 10y; SD 3y 11mo) with CP (Gross Motor Function Classification System level V) participated in this cross-sectional study. Children were excluded if they had a known metabolic disorder, genetic syndrome, or chromosomal abnormality.

Body composition changes in female adolescents with anorexia nervosa.

Background: Body weight provides limited information about nutritional status of patients with anorexia nervosa (AN).

Objectives: Our objectives were to determine body composition (BC) changes, to find clinical predictors and endocrine correlates of total body protein (TBPr) depletion, and to compare results on fat mass (FM) obtained with anthropometry (skinfold measurements) and dual-energy X-ray absorptiometry (DXA) in patients with AN.

Design: Body weight, body mass index (BMI; in kg/m(2)), BC (with DXA and skinfold measurements), and TBPr [with in vivo neutron activation analysis (IVNAA)] was assessed in 50 AN patients (15.

Longitudinal analysis of resting energy expenditure in patients with cystic fibrosis.

Objective: To assess whether elevated resting energy expenditure (REE) in female patients with cystic fibrosis (CF) persists longitudinally during late childhood and puberty.

Study Design: REE and body composition were measured 3 times in 2 years in 86 children with CF. Pubertal status, bacterial colonization, liver disease, pancreatic and pulmonary function, and genotype were determined, and linear mixed model analyses were used to determine predictors and changes in REE longitudinally.

Total body protein in healthy adolescent girls: validation of estimates derived from simpler measures with neutron activation analysis.

Background: Little recent and accurate information about body protein content in healthy adolescent girls is available.

Objective: The objective was to assess the total body nitrogen (TBN) and total body protein (TBPr) contents of fat-free mass (P:FFM) in a group of healthy adolescent girls and to validate previously published TBN prediction equations.

Design: TBN was measured with in vivo neutron activation analysis (TBNNAA).

Reduced body protein in children with spastic quadriplegic cerebral palsy.

Background: No studies have directly measured body protein or validated skinfold-thickness anthropometry and dual-energy X-ray absorptiometry (DXA) to assess body protein in children with spastic quadriplegic cerebral palsy (SQCP).

Objective: We aimed to measure and evaluate body protein and to determine whether skinfold-thickness anthropometry and DXA can predict body protein in children with SQCP.

Design: This was a cross-sectional study of 59 children (22 girls, 37 boys) aged 3.

Dietary management of galactosemia.

Galactosemia is detected by newborn screening in New South Wales and managed by the metabolic team at the Children's Hospital at Westmead. Infants with the Duarte variant are not treated. Management is based on the Handbook for Galactosemia prepared in 1998.

Differences in resting energy expenditure between male and female children with cystic fibrosis.

Objectives: To evaluate which factors might contribute to raised resting energy expenditure (REE) in patients with cystic fibrosis (CF).

Study Design: REE and anthropometry were measured in 134 (males = 68) children with CF and 100 (males = 51) controls (range, 3-18.7 years) in an outpatient setting.