A Novel Case of Marfan Syndrome in an Infant With Hypoplastic Left Heart Syndrome.

This report describes a case of hypoplastic left heart syndrome (HLHS) and Marfan syndrome presenting in conjunction, and highlights how a connective tissue disorder may alter medical and surgical management of newborns with HLHS.

Global longitudinal cardiac strain and strain rate for assessment of fetal cardiac function: novel experience with velocity vector imaging.

Background: Cardiac strain and strain rate are new methods to quantitate fetal cardiac function. Doppler-based techniques are regional measurements limited by angle of insonation. Newer feature-tracking algorithms permit angle independent measurements from two-dimensional datasets.

Use of the monoplane intracardiac imaging probe in high-risk infants during congenital heart surgery.

Unlabelled: Imaging options are limited in high-risk infants with small or abnormal oropharyngeal anatomy during congenital heart surgery.

Methods: All cases in which the monoplane intracardiac echo probe was used for transesophageal intraoperative imaging over a 15-month period at a single institution were reviewed.

Results: Eleven patients underwent intraoperative imaging using the intracardiac probe.