Publications by authors named "J P Kuebler"
Article Synopsis
- Biliary atresia (BA) is a rare liver disease in newborns that often goes unnoticed at first.
- Researchers in Germany looked at blood samples from newborns to see if they had different amino acids if they later got diagnosed with BA.
- They discovered that some babies with BA had certain amino acids at higher levels shortly after birth, suggesting the disease may start before they show symptoms, which could help in early detection.
Article Synopsis
- In 2022, the Biliary Atresia and Related Diseases (BARD) community developed a standardized definition for diagnosing cholangitis in biliary atresia (BA) patients, which was then assessed in a study involving data from 2010 to 2020 at two medical centers.
- The study found that out of 185 BA patients, 32% experienced at least one episode of cholangitis in the first year after surgery, and there was a strong correlation (0.8) between the new standardized definition and the doctors' clinical diagnoses.
- The results indicate that while the standardized definition coincided closely with clinicians' assessments, a prospective study is recommended to further refine this definition for better future diagnoses.
Introduction: Dismembered laparoscopic pyeloplasty (LP) is a well-accepted treatment modality for ureteropelvic junction obstruction (UPJO) in children. However, its efficacy and safety in infants, particularly neonates, remain uncertain. To address this significant knowledge gap, we aimed to compare outcomes between a cohort of neonates and infants undergoing LP vs.
View Article and Find Full Text PDFObjectives: Choledochal malformation (CM) is a rare disease that can lead to malignancy and potential long-term sequelae despite surgical resection. There is no long-term follow-up data on patients after CM resection in Germany. We aimed to determine the long-term outcome of our patients with a duration of follow-up >10 years and focused on long-term sequelae and health-related quality of life (HRQOL).
View Article and Find Full Text PDF