Publications by authors named "J H Ralph"
Objectives: To report a case of adult-onset non-dystrophic myotonia complicated by recurrent episodes of laryngospasm.
Methods: The patient is a 35-year-old man who was admitted to our hospital for recurrent episodes of apnea requiring endotracheal intubation with mechanical ventilation. He underwent extensive evaluation, including EMG, laryngoscopy, muscle biopsy, and genetic testing, which revealed a diagnosis of non-dystrophic myotonia.
Article Synopsis
- High medication non-adherence rates (52-73%) in pediatric stem cell transplant patients create significant health risks, motivating the development of a mobile health app.
- The BMT4me© app was designed using feedback from caregiver-child dyads and healthcare providers through interviews and focus groups, ensuring user-centered improvements.
- Usability testing showed a high SUS score of 84.2 from healthcare providers, indicating the app's effectiveness in enhancing engagement and safety for families managing pediatric transplant care.
Key Associations Found in the Struggle With Sleep in Lung Transplant Recipients.
Prog Transplant
December 2024
Introduction: Gaps exist in the understanding of the etiology of poor sleep quality after lung transplantation. Research Question: What factors are associated with poor sleep quality in lung transplant recipients?
Design: A quantitative, single-site, cross-sectional study used an anonymous survey based on 3 scales. The Pittsburgh Sleep Quality Index scale with scores dichotomized to poor versus good sleepers based on the cutoff score > 8.