[Rare case of congenital transsphenoidal meningoencephalocele causing respiratory problems].

Introduction: Congenital meningoencephalocele is a rare and severe malformation.

Aims: The authors describe the case of congenital, basal transsphenoidal meningoencephalocele associated with other neurological malformations, which projected between the margins of palatoschisis producing respiratory problems at neonatal age.

Method: Presented with detailed photo-documentation.