CLAPO syndrome: Effective response to treatment with oral rapamycin.

CLAPO syndrome (Capillary vascular malformation of the lower lip, Lymphatic malformations of the head and neck, Asymmetry and Partial or generalized Overgrowth) is a nonfrequent pathology. This syndrome is characterized by the capillary malformation (CM) of the lower lip, a very important clinical sign when diagnosing CLAPO. The aim of our report is to demonstrate that rapamycin could be a reliable and safe targeted therapy in lymphatic malformations (LMs).

[Bronchoplastic surgery: tumorectomy in principal left bronchial tube in a 5-month old child].

Introduction: Resection of bronchial tumors usually needs resection of the lung parenchyma ventilated by the ill bronchus. Surgery over a developing child must preserve the biggest amount of lung parenchyma as possible. We show a complete resection of a benign tumor from the left main-stem bronchus, without pneumonectomy.

[Management of pediatric iatrogenic tracheobronchial lesions in pediatric patients].

Aim: To present our experience in the management of three cases of tracheobronchial iatrogenic injuries and the literature revision about this pathology.

Material And Methods: We present 3 patients treated in our center with tracehobronchial iatrogenic injuries since 2005.

Results: Case 1.

Fine-needle aspiration cytopathology in the diagnosis of Wilms tumor.

BACKGROUND/PURPOSE The International Society of Paediatric Oncology (SIOP) protocol for Wilms tumor (WT) includes preoperative chemotherapy as the initial approach. However, an inadequate treatment may be performed in case of histological misdiagnosis. We evaluated the impact of fine-needle aspiration cytopathology (FNAC) in the diagnosis of unilateral WT in our group of patients.