Energy metabolism in infants with cystic fibrosis.

Objective: To determine whether a defect in energy metabolism exists in infants with cystic fibrosis (CF).

Design: Unselected, newly-diagnosed subjects with CF (n = 46) and 24 healthy infants aged <20 weeks had measurements of resting energy expenditure (REE), total energy expenditure (TEE) (n = 25), and body composition. Metabolizable energy intake (MEI) was calculated.