Homozygous familial hypercholesterolemia: Summarized case reports.

Background And Aims: Homozygous familial hypercholesterolemia (hoFH) is a rare genetic disorder with potential severe atherosclerosis in the pediatric age.

Methods: We report on 9 patients with hoFH, who had been diagnosed within the last 30 years and who were consequently treated with apheresis and drugs.

Results: Two deaths occurred: one at age 36 years and the other at age four and a half years before effective treatment was commenced.

Six-minute walk distance in overweight children and adolescents: effects of a weight-reducing program.

Objective: To assess the significance of consecutive six-minute walk tests (6MWTs) during a weight reduction program.

Study Design: Overweight children and adolescents (n = 113; mean ± standard deviation age, 12.9 ± 2.

Six-minute walk test in children and adolescents.

Objective: To evaluate the 6-minute walking distance (6MWD) for healthy Caucasian children and adolescents of a population-based sample from the age of 3 to 18 years.

Study Design: Two hundred and eighty boys and 248 girls completed a modified test, using a measuring wheel as incentive device.

Results: Median 6MWD increased from the age of 3 to 11 years in boys and girls alike and increased further with increasing age in boys (from 667.

FTIR kinetic, product, and modeling study of the OH-initiated oxidation of 1-butanol in air.

A kinetic and product study was performed on the reaction of OH radicals with 1-butanol in a 480 L indoor photoreactor and also in the EUPHORE outdoor smog chamber in Valencia, Spain. Long path in situ FTIR spectroscopy and gas chromatography with photoionization detection were used to analyze reactants and products. Using a kinetic relative rate technique, a rate coefficient of k(OH + 1-butanol) = (8.