Publications by authors named "H Zellweger"

To improve the resource utilization, reduce the pollution generation, and increase the economic benefits of enterprises, a cleaner process to produce cassava starch was proposed based on potato starch processing, and it was applied to the transformation of a traditional cassava starch processing factory in the Guangxi Province in China. The transformation involves the implementation of several new techniques/facilities, including a rasper, horizontal centrifuge, and hydrocyclone. Based on the transformation, typical cassava starch factories in Guangxi were evaluated.

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Patients with the autosomal dominant ble-pharo-cheilo-dontic (BCD) syndrome have ectropion of lower eyelids, distichiasis of upper eyelids, euryblepharon, bilaterally cleft lip/palate, oligodontia, and conical crown form. Initially known under the eponym "Elschnig syndrome" (1912), BCD syndrome has been described in binary, ternary, and quaternary combination. There is overlap with the syndrome reported by Martínez et al.

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The history of the peroxisomal disorders (PDs), including the most frequent variant, the cerebrohepatorenal syndrome of Zellweger, can be divided into four phases. During the first phase, lasting from 1964 to 1972, the clinical and pathologic manifestations of Zellweger's syndrome (ZS) were explored and delineated. In 1973 it was found that ZS is due to the absence of peroxisomes in hepatocytes and renal tubular epithelial cells.

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