Pentalogy of Cantrell: Reconstructive Challenges of Two Complete Cases in a Resource-Constrained Setting.

Pentalogy of Cantrell (POC) is a very rare congenital anomaly and treatment has remained a challenge worldwide owing to extensive reconstructive surgeries, more so in resource-constrained settings. We, therefore, report two cases of complete POC. Both successfully underwent planned reconstructions by a multidisciplinary team.

A Case of Retroperitoneal Malignant Triton Tumor in a Nigerian Boy.

Malignant peripheral nerve sheath tumor is a rare tumor occurring in 5%-10% of all malignant soft tissues sarcomas and triton tumor arising from neurofibromatosis type 1 (NF-1) is even rarer with associated high rate of mortality. No case of triton tumor has been reported in Nigeria to the best of our knowledge. We seek to report a case of lately detected retroperitoneal triton tumor presenting in a 12-year-old Nigerian child who was brought with bilateral lower limb weaknesses, weight loss, and a right lumbar mass.

Ruptured omphalocele in thoracoomphalopagus conjoined twins.

A ruptured omphalocele is a very rare complication in conjoined twins. Some cases have prompted emergency neonatal separation of the twins with varying results. We report a case of ruptured omphalocele in a thoraco-omphalopagus twin managed by primary repair of the defect at the University of Nigeria Teaching Hospital, Enugu.

The burden of pediatric malignant solid tumors in a developing country.

Objective: This study evaluates the burden of pediatric malignant solid tumors (PMST) in southeastern Nigeria.

Methods: Analysis of 174 cases of PMST managed at the University of Nigeria Teaching Hospital Enugu, from January 2002 to November 2007.

Results: PMST comprised 2.