[Classification of vascular tumours and vascular malformations. Contribution of the ISSVA 2014/2018 classification].

The study of vascular anomalies, "angiomas", vascular tumours and vascular malformations is made difficult by the great variety and confusion of the names used in the literature for these diseases, some of which are rare. The great merit of the classification proposed by the International Society for the Study of Vascular Anomalies (ISSVA), adopted in 2014 and modified in 2018, is to propose a unambiguous nomenclature and to try to group these lesions in a logical way, contrasting with the lists of the usual "classifications". This classification is based on the distinction between proliferative lesions (tumours and reactive lesions) and those which are due to a congenital anomaly of vascular morphogenesis (vascular malformations).

[Nevoid acanthosis nigricans or RAVEN (rounded and velvety epidermal nevus): three cases].

Background: We report three cases of a peculiar rash with mixed clinical features of both epidermal nevus and acanthosis nigricans. Their characteristics have been compared to those of very rare but similar cases found in the medical literature.

Patients And Methods: Two young adults (one male, one female) and a 7-year-old boy consulted for hyperchromic asymptomatic plaques located respectively on the right scapula, the left upper arm and the right frontotemporal area of the face.

[PELVIS/SACRAL syndrome with livedoid haemangioma and amniotic band].

Background: PELVIS or SACRAL syndrome denotes the association of local haemangioma and malformation in the pelvic region. In this paper, we report a case noteworthy on account of the initially livedoid appearance of the haemangioma as well as associated amniotic banding of an upper limb.

Patients And Methods: A newborn male infant underwent left colostomy on the day of birth due to anal imperforation and anomalies of the external genital organs with sexual ambiguity.

[Arteriovenous malformations: a study of 200 cases].

Objective: The aim of this study was to analyze the natural history of arteriovenous malformations by reviewing 200 consecutive cases observed in all localizations between 1992 and 1996 in a multidisciplinary angioma clinic.

Patients And Methods: Files concerning 200 arteriovenous malformations were reviewed with a standardized observation sheet applying the severity criteria defined by the International Society for the Study of Vascular Anomalies. We used the Schobinger staging system which includes 4 grades of severity: grade I=dormancy, grade II=expansion, grade III=destruction, grade IV=cardiac decompensation.