Repair of left ventricular inflow tract lesions in Shone's anomaly: valve growth and long-term outcome.

Background: The degree of involvement of left ventricular inflow tract obstruction is the predominant factor determining outcome in Shone's anomaly. In this series of patients with Shone's anomaly, we evaluated the impact of mitral valve (MV) repair strategies performed to correct the components of this anomaly on growth of the valve and long-term functional outcome in children.

Methods: In the last 25 years, 45 children, mean age 5.

Surgical correction of ascending aortic aneurysm and aortic valve incompetence by relocation of the aortic valve plane using a short aortic replacement graft.

Background: Ascending aortic aneurysms grow circumferentially and longitudinally. This geometric dislocation with widening, flattening, or loss of the sinotubular junction by aortic dilatation distorts and causes incompetence of even a structurally normal valve. We described a technique of surgical correction of ascending aortic aneurysm and valve incompetence by relocating the displaced aortic annulus plane to its normal anatomic position.

Sustained improvement after combined anterior mitral valve leaflet retention plasty and septal myectomy in preventing systolic anterior motion in hypertrophic obstructive cardiomyopathy in children.

Objective: Anatomic alterations of the mitral valve such as increased mitral leaflet area, length and laxity, and anterior displacement of the papillary muscles in hypertrophic obstructive cardiomyopathy predispose patients to residual systolic anterior motion and persistence of outflow obstruction and mitral regurgitation after septal myectomy. We investigate the long-term results of combined anterior mitral leaflet retention plasty and septal myectomy in children with hypertrophic obstructive cardiomyopathy.

Methods And Results: Anterior mitral leaflet retention plasty and subaortic septal myectomy were performed in 12 children (mean age 10.

Staged surgical palliation in hypoplastic left heart syndrome and its variants.

Background: Surgical options for infants with hypoplastic left heart syndrome (HLHS) and/or its variants are cardiac transplantation or the heart-preserving staged palliation with Norwood operation,followed by a two-staged Fontan procedure. We describe our 17-year experience with staged palliation of HLHS and/or its variants.

Methods: Between December 1989 and December 2006, 64 patients with HLHS and/or its variants underwent a Norwood procedure (mean age/weight, 11.

Isolated giant aortic aneurysm in an infant: Ehlers-Danlos syndrome type IV.

This report describes a successful surgical treatment of an isolated giant aneurysm of the ascending aorta and its arch in an 8-month-old infant.

Retrosternal compression seven years after surgical correction of partial anomalous pulmonary venous connection: Scimitar syndrome.

Seven years after surgical correction of Scimitar syndrome, a 19-year-old patient complained of progressive dyspnea and tachycardia. Transthoracic echocardiography revealed a mass compressing the right ventricle. Magnetic resonance tomogram showed its exact retrosternal location and nature.