Isolated pseudohypoplasia of the right ventricle.

We present a case of a 12-year-old girl with severe cyanosis due to abnormal moderator band producing a hidden trabecular component of the right ventricle, mimicking isolated hypoplasia of the right ventricle. A marked hypoplasia was confirmed by echocardiography and catheterization. At operation an anomalously thickened moderator band obstructing the apical infundibulum was found.

[Ectopia cordis and cardiac anomalies].

Ectopia cordis is a rare disease that occurs in 5.5 to 7.9 per million live births.