Quantifying the Effects of Hip Surgery on the Sphericity of the Femoral Head in Patients with Mucopolysaccharidosis Type I.

Background: The introduction of stem cell transplantation has improved life expectancy and cognitive outcome in patients with mucopolysaccharidosis I, but this condition remains associated with substantial residual disease in several parts of the body. Many patients have hip dysplasia with progressive medial flattening of the femoral head. Quantitative evidence on the effect of surgery on remodeling to sphericity of flattened femoral heads is lacking.

Correction to: The value of postmortem computed tomography in paediatric natural cause of death: a Dutch observational study.

When first published, this article inadvertently listed the Dutch NODO group individually within the author list without specifying the names of the collaborators. The collaborators have been listed within the Acknowledgements section only. The corrected author list is presented in this Correction.

The value of postmortem computed tomography in paediatric natural cause of death: a Dutch observational study.

Background: Postmortem CT is a relatively new field of interest within paediatric radiology. This paper focusses on its value in cases of unexpected natural death.

Objective: We report on an observational Dutch study regarding the value of postmortem CT in children with an assumed natural unexpected death because postmortem CT is part of the Dutch NODO (additional investigations of cause of death) procedure.

Prevalence of vertebral pars defects (spondylolysis) in a population with osteogenesis imperfecta.

Study Design: We performed a retrospective study of spinal roentgenograms of a large cohort of patients suffering from osteogenesis imperfecta.

Objective: To determine the prevalence of vertebral pars defects (spondylolysis) in patients with osteogenesis imperfecta.

Summary Of Background Data: Patients suffering from osteogenesis imperfecta are known to be prone to pathologic fractures.

Reliability of voiding cystourethrography to detect urethral obstruction in boys.

Objectives: To evaluate the reliability of voiding cystourethrography (VCUG) to diagnose infravesical obstruction in boys.

Methods: Hard copies of the VCUG findings of 72 boys were assessed by two pediatric radiologists and two pediatric urologists. The investigators were instructed to consider six items related to infravesical obstruction: vesicoureteral reflux, bladder wall thickness, bladder diverticulum, abnormal prostatic urethra, visible urethral obstruction, and obstruction in the sphincter area.