Rev Belge Med Dent (1984)
February 2005
We report dental anomalies related to the Bloch- Sulzberger Syndrome better known as Incontinentia Pigmenti (IP). IP is an X related hereditary disease that occurs for about 95% of all patients in females and is lethal for the male foetus. Because of severe skin lesions in the neonatal period the disease is more known by dermatologists than dentists.
View Article and Find Full Text PDFRev Belge Med Dent (1984)
February 2005
This case report represents a child that needed, at the age of 3, dental treatment under narcosis due to nursing bottle caries including multiple extractions. Six months later the few remaining teeth were again seriously affected by decay. Due to the medical history of urological problems, abnormal aspect of hair and skin and abnormal forms of primary teeth (only reported by the parents), there was a presumption of ectodermal dysplasia, so the patient was referred to the department of medical genetics.
View Article and Find Full Text PDF