Speech and language outcomes in children with auditory neuropathy/dys-synchrony managed with either cochlear implants or hearing aids.

The aim of this study was to assess the receptive language and speech production abilities of a group of school-aged children with auditory neuropathy/dys-synchrony-type hearing loss. Ten children who had received a cochlear implant in one or both ears participated. Findings for this group were compared with those for a matched cohort of implanted children with other forms of sensorineural hearing loss and with those for a group of auditory neuropathy/dys-synchrony children who were long-term hearing aid users.

Cochlear implantation in children with keratitis-ichthyosis-deafness (KID) syndrome: outcomes in three cases.

Three children with keratitis-ichthyosis-deafness (KID) syndrome received cochlear implants at the Royal Victorian Eye and Ear Hospital. KID syndrome is a rare genodermatosis associated with mutation of the connexin-26 gene with characteristics affecting skin, hair, vision and hearing. Ichthyotic involvement of the ear canal epithelium and associated non-erosive keratosis obturans complicate hearing assessment and aid fitting.

Speech perception in children using cochlear implants: prediction of long-term outcomes.

A group of 102 children using the Nucleus multichannel cochlear implant were assessed for open-set speech perception abilities at six-monthly intervals following implant surgery. The group included a wide range of ages, types of hearing loss, ages at onset of hearing loss, experience with implant use and communication modes. Multivariate analysis indicated that a shorter duration of profound hearing loss, later onset of profound hearing loss, exclusively oral/aural communication and greater experience with the implant were associated with better open-set speech perception.

Speech perception in children with auditory neuropathy/dyssynchrony managed with either hearing AIDS or cochlear implants.

Objective: To evaluate speech perception skills in children with auditory neuropathy (AN)/auditory dyssynchrony (AD)-type hearing loss managed with either hearing aids or cochlear implants.

Study Design: Prospective data collection in 3 subject groups: AN/AD children fitted with bilateral amplification, AN/AD children fitted with cochlear implant (in 1 or both ears), and a matched control group of implanted children with sensorineural hearing loss.

Main Outcome Measure: Open-set monosyllabic words (consonant-nucleus-consonant).

Receptive language and speech production in children with auditory neuropathy/dyssynchrony type hearing loss.

Objective: The purpose of this study was to characterize the receptive language and speech production abilities of school-aged children with auditory neuropathy/dyssynchrony (AN/AD) and to compare those abilities to children with sensorineural (SN) hearing loss of similar age and degree of hearing loss.

Design: Standardized speech and language tests were carried out on 12 AN/AD children, aged between 57 and 167 mo. Each of these subjects was a full-time hearing aid user or had been just before testing.

Speech perception outcomes in older children who use multichannel cochlear implants: older is not always poorer.

Speech perception outcomes for early-deafened children who undergo implantation as teenagers or young adults are generally reported to be poorer than results for young children. It is important to provide appropriate expectations when counseling adolescents and their families to help them make an informed choice regarding cochlear implant surgery. The considerable variation of results in this group makes this process more difficult.