Publications by authors named "Elizabeth A Secord"

Purpose: The United States Immunodeficiency Network (USIDNET) patient registry was used to characterize the presentation, genetics, phenotypes, and treatment of patients with Hyper IgM Syndrome (HIGM).

Methods: The USIDNET Registry was queried for HIGM patient data collected from October 1992 to July 2015. Data fields included demographics, criteria for diagnosis, pedigree analysis, mutations, clinical features, treatment and transplant records, laboratory findings, and mortality.

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Background: Little is known about the epidemiology or risk factors for oral human papillomavirus (HPV) in HIV-infected youth. The objectives of this study were to determine the prevalence and correlates of oral HPV infection and to explore the association between HPV vaccination and oral infection in HIV-infected youth.

Methods: Youth 12 to 24 years of age with behaviorally acquired HIV were recruited for this cross-sectional study.

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Background: A variety of syndromes are known to be associated with immune deficiency, some as a major part of the syndrome and some as an occasional finding.

Objectives: To report a newly defined syndrome of hydrocephalus, hypoplastic sinuses, cartilaginous webbing of the bronchi, bronchiectasis, and hypogammaglobulinemia with functional antibody deficiency in identical twin girls.

Methods: Spirometry, radiography, computed tomography (CT), bronchoscopy, and laboratory tests were performed for diagnosis.

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Background: Common variable immunodeficiency (CVID) represents a group of heterogeneous, still undifferentiated, syndromes that are all characterized by defective antibody formation. It is often associated with autoimmune disease.

Methods: An African-American girl was diagnosed with CVID at age 3 years.

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