Publications by authors named "Eddie Edwina C Landau"
This is the final of four papers updating standards for the care of people with CF. That this paper "Planning a longer life" was considered necessary, highlights how much CF care has progressed over the past decade. Several factors underpin this progress, notably increased numbers of people with CF with access to CFTR modulator therapy.
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- - This paper is part of a series updating standards of care for cystic fibrosis (CF), emphasizing the importance of recognizing and managing various CF health issues despite advancements like CFTR modulators.
- - It highlights the need for multidisciplinary care to address ongoing extrapulmonary issues such as diabetes, liver disease, and increased cancer risk, which require regular screenings.
- - Mental and emotional support is crucial for individuals with CF and their families, especially during challenging times, and planning for end-of-life care should be approached with sensitivity and compassion.
Article Synopsis
- Advances in cystic fibrosis (CF) diagnosis focus on improvements in newborn bloodspot screening, gene analysis, and understanding CFTR-related disorders.
- These developments highlight the importance of timely and accurate diagnosis for access to variant-specific therapy, which can significantly benefit those with eligible CFTR gene variants.
- The guidance in this paper updates previous standards and emphasizes the growing necessity for proper diagnosis as future trials for variant-specific therapies are anticipated.