Publications by authors named "E A Robberecht"
Article Synopsis
- The study evaluated the safety and effectiveness of a pre-emptive transjugular intrahepatic portosystemic shunt (TIPS) procedure to prevent complications from portal hypertension (PHT) in pediatric patients with cystic fibrosis-related liver disease (CFLD).
- Seven patients underwent the procedure, which was technically successful, showing a long-term patency of over 10 years and no instances of variceal bleeding during a median follow-up of 9 years.
- Despite the promising results, the progression of liver damage and related issues suggests that the overall benefits of early TIPS may be limited, leading to the discontinuation of the procedure in this context after 2013.
Background: Malnutrition is both a frequent feature and a comorbidity of cystic fibrosis (CF), with nutritional status strongly associated with pulmonary function and survival. Nutritional management is therefore standard of care in CF patients. ESPEN, ESPGHAN and ECFS recommended guidelines to cover nutritional management of patients with CF.
View Article and Find Full Text PDFBackground: Distal intestinal obstruction syndrome (DIOS) is a specific complication of cystic fibrosis.
Methods: A study was performed in 10 countries to prospectively evaluate the incidence, associated factors, and treatment modalities in children and adults.
Results: 102 patients presented 112 episodes.
Cystic fibrosis-related liver disease (CFLD) is diagnosed using a combination of criteria. Transient elastography (TE), an ultrasonographic method to evaluate liver stiffness, can differentiate patients with and without liver disease. This retrospective study (2007-2013) aimed to detect developing CFLD using consequent TE measurements.
View Article and Find Full Text PDF