Publications by authors named "Doug Y Mah"

Article Synopsis
  • - Atrial standstill (AS) is a rare condition marked by lack of electrical activity in the heart's atria, and this study aims to explore its clinical features, genetic causes, and patient outcomes.
  • - The research involved 20 patients diagnosed with AS at an average age of 6.6 years, revealing a high prevalence of arrhythmias (80%) and significant cardiac events, including cardiac arrests in 4 patients.
  • - Genetic testing showed SCN5A variants in 65% of patients, indicating that these variants may contribute to AS; patients unable to pace their atria face increased risks for blood clots, emphasizing the need for anticoagulant treatment.
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Objective: This study evaluates the ability of experienced pediatric electrophysiologists (EPs) to reliably classify incomplete right bundle branch block (IRBBB) and assesses its clinical utility as an isolated ECG finding in a group of healthy outpatient children without prior cardiac evaluation.

Design: We performed a retrospective analysis of all electrocardiographic and echocardiographic records at Boston Children's Hospital between January 1, 2005, and December 31, 2014. Echocardiographic diagnoses were identified if registered between the date of the index electrocardiogram and the ensuing year.

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Background: Implantable cardioverter defibrillators (ICDs) used to prevent sudden cardiac arrest in children not only provide appropriate therapy in 25% of patients but also result in a significant incidence of inappropriate shocks and other device complications. ICDs placed for secondary prevention have higher rates of appropriate therapy than those placed for primary prevention. Pediatric patients with primary prevention ICDs were studied to determine time-dependent incidence of appropriate use and adverse events.

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Purpose: The aim of this study is to determine if there has been a true, absolute, or apparent relative increase in congenital diaphragmatic hernia (CDH) survival for the last 2 decades.

Method: All neonatal Bochdalek CDH patients admitted to an Ontario pediatric surgical hospital during the period when significant improvements in CDH survival was reported (from January 1, 1992, to December 31, 1999) were analyzed. Patient characteristics were assessed for CDH population homogeneity and differences between institutional and vital statistics-based population survival outcomes.

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