Publications by authors named "Dora Haag"
The epidemiology of pulmonary hypertension (PH), especially pulmonary arterial hypertension (PAH), has not been evaluated in our country, therefore there is no reference parameter to establishing the representativeness of this information in the national order. This registry represents the first collaborative effort to provide a knowledge base of this disease, including 5 scientific societies that represent different specialties (pediatrics, rheumatology, pulmonology and cardiology) with data from 23 Argentine provinces. These efforts involved five societies of various adult (cardiology, rheumatology, and pulmonology) and pediatric (cardiology) specialties.
View Article and Find Full Text PDF• Pediatric pulmonary arterial hypertension (PAH) is a rare condition. • The diagnostic algorithm in PAH is key to address rare pathology and make a diagnosis. • Portosystemic shunt is a rare anomaly of the mesenteric vasculature.
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- The study investigated the effects of treprostinil on neonates with congenital diaphragmatic hernia and persistent pulmonary hypertension after one week of treatment, focusing on changes in the oxygenation index and other clinical outcomes.
- In a quasi-experimental design, 17 neonates were treated and monitored; results showed significant improvement in oxygenation, with 15 out of 17 patients surviving post-treatment, although some still had severe pulmonary hypertension.
- While treprostinil was generally well tolerated, some patients experienced adverse effects, and it suggested the need for further research to identify which patients might benefit the most from the treatment.
The aim of this study was to determine practice patterns and inter-institutional variability in how acute vasoreactivity testing (AVT) is performed and interpreted in pediatrics throughout the world. A survey was offered to physicians affiliated with the Pediatric & Congenital Heart Disease Taskforce of the Pulmonary Vascular Research Institute (PVRI), the Pediatric Pulmonary Hypertension Network (PPHNET), or the Spanish Registry for Pediatric Pulmonary Hypertension (REHIPED), from February to December 2016. The survey requested data about the site-specific protocol for AVT and subsequent management of pediatric patients with idiopathic pulmonary arterial hypertension (IPAH) or heritable PAH (HPAH).
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- Cancer can develop after solid organ transplants, particularly due to viral infections, with HHV-8 causing Kaposi's sarcoma (KS).
- A case is presented of a 15-year-old girl who developed visceral KS rapidly following lung transplantation, with lesions found in multiple organs but not on the skin.
- The report emphasizes the need for increased awareness among pediatric transplant teams about this rare complication, especially since the patient was not tested for HHV-8 before the transplant.
Pulmonary vascular disease in children is multifactorial and heterogeneous. While it shares some features with pulmonary hypertension in adults, there are differences in the associated comorbidities and conditions, the coexistence of genetic or developmental diseases. Interstitial lung diseases may be responsible for this entity.
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