Connective tissue nevi: an entity revisited.

Background: Connective tissue nevi (CTN) may be isolated, either sporadic or hereditary, or syndromic as in the Buschke-Ollendorff syndrome. Few publications have addressed the variable clinical and histopathologic expression of these benign hamartomas.

Objective: We sought to characterize the clinical and histopathologic features of CTN and to highlight a spectrum of clinical disease.

Fibroblastic rheumatism: fibromatosis rather than non-Langerhans cell histiocytosis.

Background: Fibroblastic rheumatism is a unique fibro-proliferative disease affecting the skin and joints. It is characterized by distinctive clinical and histological features related to benign spindle-shaped cells proliferation. Pediatric reports are scarce in the literature.