[Carbohydrate-deficient glycoprotein syndrome and progression in electrophysiological results].

Purpose: To document the progression of clinical and electrophysiological abnormalities in an infant with carbohydrate-deficient glycoprotein syndrome type Ia (CDGS Ia) over a period of 5 years.

Patient And Methods: A 12-month-old male underwent clinical ophthalmic and electrophysiological examination at the age of 1, 2, and 6 years. Neurological examination, magnetic resonance imaging of the brain and a genetic study were also undertaken.

[Value of the Bébé-Vision test in the screening of strabismus and anisometropic amblyopia in infants].

Purpose: To evaluate the accuracy of the Bébé-Vision test for detecting strabismic, ametropic and anisometropic amblyopia in childhood.

Methods: We screened 199 infants under 20 months of age. The screening consisted of a full orthoptic examination by a trained orthopist (cover test, fixation test), a forced choice preferential looking technique (Bébé-Vision test) prior to cycloplegia to test visual acuity, cycloplegic refraction by retinoscopy, and examination of the fundi.

[Cure of oculomotor paralysis with a muscle relaxant (Baclofen)].

The authors report a case of oculomotor palsy, whose symptoms resolved after administration of a muscle relaxant: Baclofène. This action appeared to be due to suppression of a reactive spasm. It may be a useful treatment for secondary diplopia, after oculomotry palsy.

[Basedow's neuropathy].

A case report of grave's neuropathy. The symptoms appeared in a treated patient when there was a biologic hypothyroidy. A total remission was observed after corticotherapy.

[The central visual field in flicker stimulation].

The authors reported their results of flicker visual field in ganzfeld and 17 central points with 3, 8, 15 and 35 Hertz flicker. They tested 4 groups of control subjects and 12 patients with glaucoma. The flicker visual field may be a useful aid in determining campimetric abnormalities for glaucoma patients with normal static perimetry.

[Oscillating algorithm in medical diagnosis : alternation of flow-charts and diary programs].

26 programs of paraclinical tests for inpatients were written in diary form. Conditions of use were clearly defined with emphasis on optimal utilization of the first two or three days of the stay. Nine diaries are presented as examples.

[Renal manifestations of Sjögren's syndrome. Review of the literature starting with a case].

Sjögren syndrome, characterized by lymphocytic proliferation and drying up of exocrine secretions ("sicca syndrome") due to glandular destruction, is well known for it's ocular and salivary localizations. However, other glandular epithelia (bronchial, vaginal . .