Transalar transsphenoidal meningoencephalocele presenting in the form of recurrent meningitis: Report of two cases and discussion of the diagnosis and treatment.

Introduction: Skull base meningoencephaloceles are rare congenital malformations. The two cases of transalar transsphenoidal malformation reported here differ from the classical transsphenoidal meningoencephalocele.

Case Reports: Case 1 was a three-and-a-half-year-old boy and case 2 was a 36-year-old man.

Cervical lymph node metastases and T1 squamous cell carcinoma of the lips.

Objective: The occurrence of cervical lymph node metastasis is a major prognostic factor for head and neck squamous cell carcinoma (SCC) of the lip. This study focuses on patients with T1 stage tumours,in order to describe the prevalence of metastatic lymphadenopathies.

Methods: A multicenter retrospective study was performed in three tertiary care referral centers and included 59 patients surgically treated for T1 stage SCC of the lips from January 1996 to December 2006.

Lateral semicircular canal fistula in cholesteatoma: diagnosis and management.

The objective of this retrospective study was to present the authors' experience on the management of labyrinthine fistula secondary to cholesteatoma. 695 patients, who underwent tympanoplasty for cholesteatoma, in a University Hospital between 1993 and 2013 were reviewed, to select only those with labyrinthine fistulas. 42 patients (6%) had cholesteatoma complicated by fistula of the lateral semicircular canal (LSCC).

Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.

Objectives: To determine the diagnostic approach to severe or profound bilateral postmeningitic deafness and to propose management guidelines.

Material And Methods: A retrospective review of five patients (two adolescents and three infants) with rapidly progressive severe bilateral deafness following an episode of meningitis managed between 2004 and 2010.

Results: The two adolescents presented Neisseria meningitidis meningitis and the three infants presented Streptococcus pneumoniae meningitis.

Treatment of earlobe keloids by surgical excision and cryosurgery.

Background: The long-term results of keloid treatments remain poor.

Objective: To assess the long-term efficacy of a technique combining surgical excision and immediate cryosurgery in patients with ear keloids.

Methods: A retrospective study was performed between January 2001 and June 2011.

BRAF mutation in papillary thyroid carcinoma: predictive value for long-term prognosis and radioiodine sensitivity.

Objectives: BRAF pV600E mutation is the most common oncogenic event and the most specific mutation for papillary thyroid carcinoma (PTC). Many studies over the last decade have shown a direct relationship between BRAF mutation and aggressive tumour characteristics, resulting in poor prognosis. However, several recent studies have suggested that BRAF mutation is not associated with poor prognosis of PTC.

Preoperative computed tomography scan may fail to predict perilymphatic gusher.

Objectives: A stapes gusher is a very rare event in ear surgery, but the consequences for hearing can be dramatic. It can usually be predicted by characteristic radiologic abnormalities. We report 2 cases of gusher without any abnormalities seen on the preoperative computed tomography scans.

Intralabyrinthine schwannomas: a case series with discussion of the diagnosis and management.

Objective: By extracting cases of intralabyrinthine schwannomas (ILS) from the sum of all vestibular schwannomas, we aim to identify and analyze unique features of its presentation. This allows us to refine the management protocol of this rare condition.

Design: This is a retrospective study of all patients seen in the Department of Otorhinolaryngology-Head and Neck Surgery, Rouen University Hospital, with either ILS or ILS with intracanalicular extension (ILS-IAC) between 2001 and 2011.

Sialendoscopy: a new diagnostic and therapeutic tool.

Background: Sialendoscopy is a recently developed minimally invasive diagnostic and therapeutic procedure for the management of obstructive diseases of the salivary glands. This report describes our early experience with this new tool and compares our results with the literature data.

Material And Methods: This was a retrospective analysis of the 33 first cases treated at a teaching hospital from October 2009 to June 2011.

Management of voice prosthesis leakage with Blom-Singer large esophage and tracheal flange voice prostheses.

Introduction: Voice rehabilitation after total laryngectomy is a major socio-economic challenge. Voice rehabilitation can be achieved by voice prostheses, which provide rapid patient satisfaction. Enlarged tracheo-oesophageal puncture is a frequent complication and can be difficult to manage.

Acquired cholesteatoma in children: strategies and medium-term results.

Objectives: To assess paediatric cholesteatoma surgical management strategies, residual disease and recurrence rates and especially the medium-term auditory impact.

Material And Methods: Retrospective study of 22 cases of acquired middle ear cholesteatoma selected from a series of 77 children under the age of 16 operated for cholesteatoma between 1st January 2000 and 31st December 2003 on the basis of the following criteria: first-line surgical management with postoperative follow-up greater than four years. Surgical strategies, preoperative and postoperative (at 1 year and at the final visit) audiograms and residual disease and recurrence rates were analysed.

Laryngeal abnormalities are frequent in the 22q11 deletion syndrome.

Objectives: The 22q11 microdeletion is a chromosomal disorder detected by fluorescence in situ hybridization (FISH). It has been known since the 80s, and is involved in many malformative syndromes (DiGeorge sequence, VCFS syndrome, etc.).

Acute mastoiditis in children: 10 years experience in a French tertiary university referral center.

Acute mastoiditis have been increasingly reported in the last decade, with bacteriologic modifications and new therapeutic guidelines. This study is a retrospective review of 36 children hospitalized for acute mastoiditis in a French tertiary university referral center from 1999 to 2009, to assess incidence, bacteriology of pathogens and management. There were 10 periosteitis and 26 subperiosteal abscesses.

Basaloid squamous cell carcinoma of the head and neck: report of 18 cases.

Objective: To evaluate the clinical course and pathological characteristics of basaloid head and neck squamous cell carcinoma.

Method: Retrospective study of 18 cases of basaloid head and neck squamous cell carcinoma. Epidemiological, clinical and histological data were analysed and the Kaplan-Meier test used to estimate survival rates.

[Thyroid differenciated carcinoma in children. Study from Normandy].

Objective: Definition of a strategy for the management of thyroid differenciated carcinoma in children.

Design And Setting: Retrospective cohort study from the Normandy area in France.

Method: Analysis of the medical records of 13 children and adolescents (age > 15 years), presenting with thyroid differenciated carcinoma in three Normandy French hospitals from 1994 to 2006, to determine the clinical features and treatment of the disease.

[Role of hypnotherapy in the treatment of debilitating tinnitus].

Objective: Hypnotherapy is currently used for tinnitus therapy in our university hospital. The aim of this study was to evaluate its efficacy.

Material And Methods: This study was performed on 110 patients suffering from distressing tinnitus.

[CT scan, MR imaging and anatomopathologic correlation in the glottic carcinoma T1-T2].

Objectives: Endoscopy and imaging are necessary to diagnose glottis carcinoma. Today, CT scan is the gold standard but MR imaging should be more sensitive for neoplastic invasion detection. The purpose of this study was to determine which exam to perform (CT scan or MRI) for neoplastic invasion.

Endoscopic revision of external dacryocystorhinostomy failure.

Objective: To evaluate the usefulness of endoscopic analysis and surgery of the lacrimal sac in cases of external dacryocystorhinostomy (DCR) failure.

Material & Method: In a retrospective study, 17 endoscopic procedures in 17 patients during 11 years with recurrent lacrimal obstruction after external DCR were performed. Endoscopic analysis and procedures were carried out with a routine silicone tube catheterization for 3 to 6 months.

Nasolacrimal duct oncocytoma: an unusual cause of chronic epiphora.

Epiphora has traditionally fallen under the purview of ophthalmologists. However, owing to the development of endoscopic dacryocystorhinostomy, this condition has been increasingly observed in otolaryngologic practice. We report the case of a woman with a 4-month history of right epiphora and dacryocystitis.

Role of radiotherapy in the treatment of nasoethmoidal adenocarcinoma.

Objective: To assess the efficacy of radiotherapy in the treatment of nasoethmoidal adenocarcinoma.

Design: Multicenter, retrospective study.

Setting: Eleven French hospitals.

Vagal paraganglioma of the neck: a case report.

Vagal paragangliomas are rare in the head and neck. Complementary use of computed tomography and magnetic resonance imaging can facilitate the diagnosis and help determine the best management approach. Most paragangliomas should be treated with surgery.

Rhinoscleroma of the sinuses.

Introduction: Rhinoscleroma is a rare chronic, granulomatous disease of the respiratory tract.

Objective: The aim of this paper was to report 2 unusual cases of rhinoscleroma and to review the literature.

Material: We present two cases of sinus rhinoscleroma diagnosed and treated at the ENT Department of a French University hospital.

Rhinoscleroma: a French national retrospective study of epidemiological and clinical features.

Background: Rhinoscleroma (RS) is a rare, chronic, granulomatous disease of the upper respiratory tract that is associated with infection with Klebsiella rhinoscleromatis. RS is more common in certain geographic regions than in others, but other risk factors and the pathogenesis of RS remain unclear.

Methods: We sent a standardized questionnaire to all pathologists and otolaryngology specialists in French University Hospitals and asked whether they had seen patients with RS in the previous 16 years (1990-2005).