Superficial Acral Fibromyxoma: Report of 13 Cases With New Immunohistochemical Findings.

Background: Superficial acral fibromyxoma (SAF) is a benign, soft tissue neoplasm preferably located on the digits.

Methods: We collected 13 cases of SAF and evaluated their clinical, histopathologic, and immunohistochemical features.

Results: This study included 9 males and 4 females, median age 54 years.

Paraneoplastic autoimmune multiorgan syndrome (paraneoplastic pemphigus) with unusual manifestations and without detectable autoantibodies.

We describe a patient with paraneoplastic autoimmune multiorgan syndrome (PAMS) secondary to a lymphoblastic T- cell lymphoma who presented with a lichenoid dermatitis and vitiligo, later developing bronchiolitis obliterans and autoimmune hepatitis. Notably, he had no detectable autoantibodies. The development of vitiligo and autoimmune hepatic involvement probably indicate a role for cytotoxic T- cell lymphocytes in the pathogenesis of this syndrome.