Congenital emphysema in children: segmental lung resection as an alternative to lobectomy.

Background: Congenital emphysema is a rare lung malformation characterized by overinflation of lung segments or lobe, together with ventilation and lung perfusion disorders. The lesion frequently causes respiratory distress in infants and may require urgent surgery. The pathogenesis is still controversial, and the usual treatment recommended is a lobectomy.

Lung aplasia: anatomy, history, diagnosis and surgical management.

Purpose: The aim of the study was to define the details of the history and clarify the cause for respiratory distress, justify the need for surgical correction and suggest a rational operative technique for patients with lung aplasia.

Methods: Our experience with the management of 9 patients with lung aplasia and 1 patient with lung agenesis in the period from 1985 to 2004 is presented. All 10 patients were referred for respiratory distress.

Endorectal pull-through for Hirschsprung's disease: 17-year review of results in Ukraine.

Several surgical procedures are available for the treatment of Hirschsprung's disease (HD) the choice often depends on the surgeon's preference. The procedure that is most convenient for the surgeon is not necessarily the optimal one for the patient, however, and complications and mortality need to be considered. We reviewed our series of 275 children operated upon for HD by endorectal pull-through after Soave-Boley dissection of the seromuscular cuff followed by a hand-sutured (HSA) (210) or stapled (SA) (65) primary perineal colorectal anastomosis.

Aplasia of the right lung in a 4-year-old child: surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome.

Lung aplasia is defined as unilateral absence of the lung with preservation of main bronchus remnant at the tracheal bifurcation. Patients usually die soon after birth and there is no specific therapy for this condition, as evidenced by the literature. The authors present a case of an infant that was asymptomatic with this malformation until 3 months of age, when the child had respiratory distress syndrome.