Evolution of a cochlear schwannoma on clinical and neuroimaging studies. Case report.

The authors report on a patient with a rare schwannoma that arose from the cochlear division of the vestibulocochlear nerve. Distinctively, the lesion appeared to arise from the cochlea itself and was monitored with clinical and neuroimaging studies for 12 years before it was diagnosed and treated. The atypical occurrence of schwannomas of the vestibulocochlear nerve originating in the inner ear structures underscores the high level of clinical suspicion required for the diagnosis of these lesions in patients presenting with persistent auditory and vestibular symptoms.

Choroid plexus papilloma and meningioma: coincidental posterior fossa tumors: case report and review of the literature.

Objective: We report an unusual case of an extraventricular choroid plexus papilloma (CPP) occupying the right ventral foramen magnum and lower right cerebellopontine angle (CPA), occurring together with a petro-tentorial meningioma. The clinical presentation, preoperative imaging, differential diagnosis, surgical treatment and histologic features of the two tumors are discussed.

Case Description: The patient presented with a 2-month history of headache, altered facial sensation, dysphagia, and gait unsteadiness.

Pediatric and adult cochlear implantation.

The frequency of cochlear implantation has increased tremendously over the past decade. Cochlear implantation is often performed as an outpatient procedure and is considered an acceptable treatment for severe to profound sensorineural hearing loss in patients who are refractory to conventional hearing augmentation. Imaging plays an important part in the work-up of cochlear implant candidates, and an understanding of imaging evaluation procedures is essential.

Autoimmune inner ear disease: diagnostic and therapeutic approaches in a multidisciplinary setting.

Autoimmune Inner Ear Disease (AIED) is a clinical syndrome of uncertain pathogenesis. It is associated with bilateral rapidly progressive hearing loss. The hearing loss may be associated with vestibular symptoms.

Outcomes of cochlear implantation in children with auditory neuropathy.

Ten children who were diagnosed with auditory neuropathy were matched with ten children who were diagnosed with other etiologies. All twenty children received cochlear implants at the Mayo Clinic in Rochester, Minnesota. Various measures were used to compare the outcomes for the two groups.

Costimulating aberrant T cell responses by B7-H1 autoantibodies in rheumatoid arthritis.

A pathogenic hallmark of rheumatoid arthritis (RA) is persistent activation of self-reactive CD4(+) T cells. The cause of this aberrant activity remains elusive. We report here detection of autoantibodies against B7-H1, a recently described member of the B7 family, in 29% of patients with RA versus 4% of healthy donors.

Significance of House-Brackmann facial nerve grading global score in the setting of differential facial nerve function.

Objective: To determine the clinical significance of the House-Brackmann facial nerve grading scale (HBFNGS) in the setting of differential function along the branches of the facial nerve.

Study Design: Prospective study of 38 patients with facial palsy who demonstrated differential facial function.

Setting: Tertiary referral center.

Isolated, giant cerebellopontine angle craniopharyngioma in a patient with Gardner syndrome: case report.

Objective And Importance: We report the case of a 29-year-old man with Gardner syndrome and an isolated, giant cerebellopontine angle craniopharyngioma. Our description of this patient is only the second case report of a craniopharyngioma arising primarily in the cerebellopontine angle.

Clinical Presentation: The patient presented with a 1-year history of progressive neurological impairment and headache.