[Current limitations and new perspectives in the diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia].

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle. In ARVC/D there is a progressive replacement of right ventricular myocardium with fatty and fibrous tissue and ventricular arrhythmias of right ventricular origin. The precise prevalence of ARVC/D has been estimated to vary between 1 in 1000 to 1 in 5000 of the general population.

[Usefulness of home monitoring in patients with implantable cardioverter-defibrillators].

During the last years several remote monitoring systems have been introduced in everyday clinical practice, because of the development of new computer and information technologies. Therefore, clinical and technical data of implanted devices can be transmitted by patients directly to the cardiology department through a transtelephonic web-based connection, without undergoing traditional outpatient evaluation. Home monitoring systems are effective in identifying device malfunctioning and clinical instability in patients with implantable cardioverter-defibrillators.