Vestibular dysfunction is a manifestation of 22q11.2 deletion syndrome.

The 22q11.2 deletion syndrome (22q11.2DS) is the second most common cause of developmental delay after Down syndrome.

Prevalence and Nature of Hearing Loss in 22q11.2 Deletion Syndrome.

Purpose: The purpose of this study was to clarify the prevalence, type, severity, and age-dependency of hearing loss in 22q11.2 deletion syndrome.

Method: Extensive audiological measurements were conducted in 40 persons with proven 22q11.