Sclerosteosis in a Spanish male: first report in a person of Mediterranean origin.

We report the first observation of sclerosteosis in Spain. To the best of our knowledge, this is the first case of sclerosteosis in a person of Mediterranean origin with no known Dutch ancestors. He has the characteristic phenotype of the disease with right facial nerve palsy and syndactyly and the typical radiological features, including generalised bone sclerosis and cortical widening of the tubular bones.

Median mandibular cleft.

We report on a patient with median cleft of mandible and lower lip and its associated corrective treatment, and we review the literature.

Priming with GHRH (1-29) NH2: an aid in differential diagnosis between hypothalamic and pituitary deficiencies.

More than 80% of children with growth hormone deficiency (GHD) respond with a rise in growth hormone levels when given 1 microgram/kg body weight of growth hormone-releasing hormone (GHRH) in an i.v. bolus.

Craniofacial treatment of giant-cell tumors of the sphenoid bone.

We report a craniofacial approach for resection of a giant-cell tumor of the sphenoid bone. Complementary radiotherapy was performed because of the incomplete tumor remotion. Four-year follow-up is presented.

[Use of autologous fibrin glue in facial reconstruction by total skin graft].

Fibrin glue of human origin was used in 12 patients following excision of facial skin tumors and reconstruction skin graft. Positive results were achieved in all cases with good by full-thickness healing, reduction of operating time and good aesthetic results.

[The costs for a health center in relation to its activities].

Objective: To establish a system of attributing costs of Health Centres (HC) in the Primary Care network in function of health care activity.

Design: Crossover study with a descriptive component.

Setting: Management.

Understanding variances in hospital stay.

Systems for tracking, analyzing, and reporting variances in the length of hospital stay enable nurse case managers, nurse managers, and nurse executives to ensure desirable clinical outcomes in a cost-effective manner.

[Magnetic resonance in Hallevorden-Spatz disease].

The Hallevorden-Spatz disease should be suspected in children or young people with motor, pyramidal or extrapyramidal symptomatology and deterioration of superior functions specially upon the existence of family history. Pathognomonic diagnosis may only be obtained by necropsy but magnetic resonance images, although not pathognomic, are sufficiently characteristics to strongly support the diagnosis. Four cases of Hallevorden-Spatz disease are presented with special emphasis on the MR images characteristic of this disease.

Congenital hemihypertrophy.

We present an isolated complete left hemihypertrophy in a girl with follow-up data from birth up to the age of 5 months.

Analysis of motor vehicle crash data in an urban trauma center: implications for nursing practice and research.

Objective: To examine the incidence of risk behaviors (safety restraint use and alcohol use) and demographic characteristics of motor vehicle crash victims.

Design: Retrospective, descriptive, correlational.

Setting: One major, urban, Level 1 trauma center.

Usefulness of serum apolipoprotein B levels for screening children with primary dyslipoproteinemias.

Objective: To assess the use of serum apolipoprotein B levels for screening children with primary dyslipoproteinemia (those with elevated levels of low-density lipoprotein cholesterol [LDL-C]) and to know the types of dyslipoproteinemias we can identify.

Design: Criterion standard.

Setting: Referral center.

Study of interactions between Listeria monocytogenes and experimental tumors.

Objective: to verify the effects of Listeria monocytogenes (LM) inoculation in the survival of animals bearing Ehrlich's tumor. KIND OF STUDY: experimental. Animals-isogenic mice, Balb/c, female, 19-21 g.

[Action of 3,5,3'-triiodothyronine (T3) on Walker's 256 carcinosarcoma development].

In order to verify the effects of triiodothyronine (T3) administration in animals bearing Walker tumor, the authors have carried out an experimental study utilizing Wistar rats inoculated with both ascitic and solid Walker tumor, and Balb/c isogenic mice for the study of spreading of macrophages. The animals were treated with T3 20 micrograms/100 g of body weight and the data were analysed by Chi-square and Mann-Whitney tests. The authors conclude that T3 increases significantly the survival of rats bearing Walker tumor, and the spreading of macrophages when inoculated into the peritoneal cavity of mice.