[Electrically evoked ABR through cochlear implant in children with auditory neuropathy spectrum disorder].

Objective: To estimate the applicability of electrically evoked auditory brainstem response (eABR) registration for the estimation of neural integrity after cochlear implantation (CI) in children with auditory neuropathy spectrum disorder (ANSD) and to compare the eABR data with patient's hearing performance.

Material And Methods: 4 children, Nucleus (Cochlear) CI users, with ANSD were enrolled in the study. Hearing performance in these children ranged from successful to unsatisfied.

[Evaluation of the cochlear implantation users rehabilitation results using psychoacoustic methods].

Unlabelled: Currently, the number of patients with bilateral sensorineural deafness treated with cochlear implantation (CI) is increasing in the Russian Federation. In this regard, methods of assessing the auditory rehabilitation of this category of patients become more relevant.

Objective: To investigate the correlation of the speech intelligibility in quiet with frequency resolving power (FRP) of hearing using a ripple-spectrum phase reversion test (RSPRT) in CI users.

[Threshold dynamics of the auditory nerve electrically evoked compound action potential in implanted children].

Objective: To study the dynamics of thresholds of the electrically evoked compound action potential of the auditory nerve (ECAP) during neural responce telemetry (NRT) intraoperatively, at the time of activation of the cochlear implantation system (CI) and after 3 and 6 months.

Material And Methods: The study included 50 children aged 1 year to 4 years with bilateral sensorineural deafness, operated on by Nucleus CI512 Profile + CP900 CI systems («Cochlear», Australia). In all patients, the electrode array was fully inserted.

[Postoperative dynamics of electrode impedance changes in children with cochlear implants].

Unlabelled: To determine the electrode impedance dynamics changes in the postoperative period after cochlear implantation as well as the time of their stabilization.

Material And Methods: 75 patients with a bilateral sensorineural deafness aged from 1 to 4 years (average age - 1.5 years) were included in the study.

[The effectiveness of the speech therapist and audiologist collaboration during speech processor fitting].

The aim of the study was to present the first clinical experience of clinical trials of new methodology of the CI speech processor fitting with the new software Nucleus Fitting Software - NFS. At all 4 fittings sessions there were 15 children. During the fitting sessions 2 techniques were used - with the new NFS software and classical technique were used.

[Evoked potentials in the rehabilitation of the patients after cochlear implantation].

The objective methods for the hearing examination of the patients after cochlear implantation provide an important tool for the speech processor fitting. The aim of the present study was to evaluate the possibilities and the informative value of the electrically evoked compound action potential (ECAP) and electrically evoked auditory brainstem response (EABR) combined recording technique. For this reason, the comparison of the ECAP and EABR thresholds with comfortable levels of stimulation, obtained on the basis of subjective response and psychophysical testing of the patients with good results after cochlear implantation was performed.

[Application of the mathematical model for prognosis in the rehabilitation of children after cochlear implantation].

Unlabelled: Despite the variety of etiological factors, cochlear implantation (CI) remains the only effective method for the rehabilitation of the patients presenting with total deafness. The aim of this study was the enhancement of the efficiency of selection of the candidates for CI, the improvement of the quality of rehabilitation of the patients with cochlear implants, and the determination of the prognostic criteria for clinical trials.

Patients And Methods: (CI).

[The Russian-language version of the matrix test (RUMatrix) in free field in patients after cochlear implantation in the long term].

Unlabelled: The deterioration of speech intelligibility in the patients using cochlear implantation (CI) systems is especially well apparent in the noisy environment. It explains why phrasal speech tests, such as a Matrix sentence test, have become increasingly more popular in the speech audiometry during rehabilitation after CI. The Matrix test allows to estimate speech perception by the patients in a real life situation.

[The impact of implantable technologies on the quality of life in the patients with hearing loss].

The improvement of the effectiveness of the rehabilitation of the patients with hearing disorders is a priority task for an audiologist. One part of the present work was to assess satisfaction of the patients treated with the use of the hearing aids, drug therapy, and the surgical operations. The aim of the study was to evaluate the influence of the implantation of the Baha bone conduction system on the quality of life of the treated patients.

[The results of cochlear implantation in the patient with hereditary and non-hereditary hearing loss].

The objective of the present study was to evaluate the effectiveness of rehabilitation of the patients after cochlear implantation in the early and late periods after operation taking into consideration the etiology of congenital deafness. The comprehensive clinico-audiological examination performed during the period from 2010 to 2015 involved 246 children who had undergone cochlear implantation (CI). All children were operated at the National Research Center for Audiology and Hearing Rehabilitation in the period from 2003 to 2013.

[Reoperations after cochlear implantation].

Unlabelled: The objective of the present study: the improvement of the quality and effectiveness of the surgical stage of cochlear implantation on the basis of the comprehensive analysis of performed reoperations.

Patients: 84 patients of the 2413 ones who had undergone cochlear implantation were re-examined by revision surgery within various periods after the first intervention.

Main Results: In certain patients, the correction of the intracochlear electrode array position was performed and in 72 cases the replacement of the implant was done.

Phenotype in a patient with p.D50N mutation in GJB2 gene resemble both KID and Clouston syndromes.

Keratitis-ichthyosis-deafness (KID) syndrome (OMIM 148210) is a rare ectodermal dysplasia syndrome characterized by vascularizing keratitis, congenital profound sensorineural hearing loss, and progressive erythrokeratoderma. We have found a 148G-A transition in the GJB2 gene, resulting in an asp50-to-asn (D50N) substitution in a girl with congenital deafness. This finding allowed us to diagnose а KID syndrome.

[The new technologies for the intraoperative registration of the electrically evoked compound action potentials of the acoustical nerve by means of the neural response telemetry method].

The present article reports the results of a clinical study of the new wireless device CR120 designed for the intraoperative registration of electrode resistance and the electrically evoked compound action potential (EAP) of the acoustical nerve by means of neural response telemetry. The study has demonstrated the high effectiveness of the application of the new wireless device in clinical practice. It was shown that the registration of electrically evoked compound action potential with the help of the CR120 Intraoperative Remote Assistant took 22% less time than by the conventional method (p<0.

Evaluation of new technology for intraoperative evoked compound action potential threshold measurements.

Objective: To determine whether new technology for intraoperative evoked compound action potential (ECAP) threshold measurements-the CR120 Intraoperative Remote Assistant device-is comparable to the existing Custom Sound(®) clinical system, as well as assess test-retest accuracy of the systems.

Design: Within subject, repeated measures comparative design.

Study Sample: ECAP data were collected from 81 pediatric subjects (41 females and 40 males).