[Cochlear implantation in immunocompromised patients].

This paper reports a clinical case that gives evidence of the possibility of cochlear implantation after liver transplantation. Patient K. aged 3 years 10 months was admitted to the Russian Research and Practical Centre of Audiology and Hearing Rehabilitation with the diagnosis of type IB glycogenosis after maternal liver transplantation associated with chronic neutropenia, chronic cutaneous and mucosal infection, partial symptomatic partial epilepsy, retarded psycho-motor development, and complaints of the absence of auditory response.

[Johanson-Blizzard syndrome: audiological features and results of cochlear implantation].

Johanson-Blizzard syndrome is a rare congenital autosomal recessive disease characterized by the association of congenital deficiency of the exocrine pancreatic function and multiple malformations. One of the most common manifestations of this pathology is sensorineural hearing loss of different severity and anomalous development of the inner ear. The case of cochlear implantation in the patient presenting with bilateral sensorineural deafness, congenital malformation of the inner ear, and stenosis of the internal auditory canal is reported.

[The audiological phenotype and the prevalence of GJB2-related sensorineural loss of hearing in the infants suffering acoustic disturbances].

The objective of the present work was to study specific features of the audiological phenotype and the prevalence of GJB2-related sensorineural hearing loss (SNHL) in the infants suffering acoustic disturbances. The study included 264 children with bilateral non-syndromic sensorineural loss of hearing diagnosed during the first year of life by means of detailed audiological examination that included tympanometry, registration of short-latency auditory action potentials (SLAAP), delayed evoked otoacoustic emission (DEOAE), distortion product-frequency otoacoustic emission (DPFOAE), and auditory brain-stem response (ABR). In addition, stationary acoustically evoked responses (SAER) were recorded in 38 children presenting with hearing impairment associated with GJB2-related sensorineural loss of hearing.

[Novel possibilities for the rehabilitation of patients presenting with congenital external and middle ear malformations].

The objective of the present study was to estimate the advantages of cochlear Baha BIA 400 abutments in the intraoperative and early postoperative periods. A total of 10 implantations of the systems with the use of hydroxyapatite bone cement were performed in 9 patients of different age. Stability of the implants and intensity of skin reactions were evaluated.

[The experience of the work of a regional cochlear implantation center].

The objective of the present study was to determine the main lines of the development of a regional cochlear implantation centre and to estimate the effectiveness of rehabilitation of the children treated with the use of cochlear implantation. Analysis of the results of the work of the branch of the Russian Research and Practical Centre of Audiology and Hearing Rehabilitation based at Voronezh Regional Children's Clinical Hospital No 1 provided materials for the establishment of the principle directions of activities of the regional cochlear implantation centre where a total of 161 children have been kept under observation during the last years. Fifty six of the 138 children at the age varying from 1 to 12 years were given the surgical treatment.

[The effectiveness of rehabilitation following bilateral cochlear implantation].

The Russian Federation similar to many other countries witnesses the continuous rise in the number of patients undergoing bilateral cochlear implantation. The objective of the present study was to estimate the effectiveness of rehabilitation following bilateral cochlear implantation. A total of 28 patients admitted to the Russian Research and Practical Centre of Audiology and Hearing Rehabilitation between 2011 and 2012 were available for the examination with the use of tonal threshold audiometry.

[The current tendencies and prospects of the neural response telemetry in the rehabilitation of the patients after cochlear implantation].

The objective of the present study was to estimate the potential of the modern technique for telemetry of the neural response during rehabilitation of the patients following cochlear implantation. The methods for the purpose included comparison of the results of intra- and postoperative registration on neural response telemetry (NRT) and evaluation of the influence of perimodiolar localization of electrodes of cochlear implants on the threshold level of stimulation and propagation of excitation inside the cochlea. The results of the study confirm the possibility of using the registration of the electrically evoked auditory nerve potential for fitting the speech processor of the cochlear implant.