[Spontaneous cerebrospinal rhinorrhea: role of computerized opaque cisternography].

Spontaneous CSF rhinorrhoea, secondary to trauma in the great majority of cases, is very rare (3-4%). The authors report a case of spontaneous CSF rhinorrhoea secondary to an ethmoidal osteodural defect, diagnosed by digital cisternography and confirmed by the surgical operation. The value of digital opaque cisternography and its place in the diagnostic arsenal are discussed.

A non-syndrome form of neurosensory, recessive deafness maps to the pericentromeric region of chromosome 13q.

Non-syndromic, recessively inherited deafness is the most predominant form of severe inherited childhood deafness. Until now, no gene responsible for this type of deafness has been localized, due to extreme genetic heterogeneity and limited clinical differentiation. Linkage analyses using highly polymorphic microsatellite markers were performed on two consanguineous families from Tunisia affected by this form of deafness.

A genetic study of otosclerosis in a population living in the north of Tunisia.

The frequency of otosclerosis has been estimated to be 0.6 per 100 inhabitants in a population living in the North of Tunisia. The sex ratio in probands is 0.

An epidemiological and genetic study of congenital profound deafness in Tunisia (governorate of Nabeul).

An epidemiological and genetic study of profound deafness has been undertaken in the governorate of Nabeul in Tunisia. This paper deals with sensorineural deafness with no associated abnormalities. The prevalence was estimated to be 0.

[Intratympanic meningioma. Apropos of a case].

A 40 year old woman presented with a meningioma of the intratympanic region, a very rare localization which raises problems of differential diagnosis from jugular glomus tumors. A brief historical survey and complete etiopathogenic study are presented, and clinical features and results of complementary examinations, particularly angiography and computed tomography, are described. Treatment is exclusively surgical and diagnosis is confirmed with certitude by histopathology only.

[Papillary carcinoma developing in thyroglossal duct cyst. Apropos of 2 cases].

The authors report two cases of papillary carcinoma of a thyreoglossal duct cyst. In both cases, the thyroïd gland was normal. Clinical manifestations are not specific and the diagnosis is usually made by histopathologic examination which reveals in the majority of cases a papillary carcinoma.

[Mondini's syndrome. Apropos of 2 cases].

Two children presented with congenital deafness from internal ear malformations of the Mondini type which had provoked recurrent attacks of meningitis due to foot of stapes fistulae. Good results were obtained after vestibular plugging. Anatomical pathways taken by the fistulae are described and certain important points emphasized.

[Early auditory evoked potentials in spinocerebellar heredodegenerative involvement].

Results of early auditory evoked potentials, recorded during exploration of spinocerebellar heredodegenerative lesions (21 cases of Friedreich's disease, 8 cases of Pierre-Marie's disease and 3 cases of Strumpell-Lorraine disease), are analyzed. Tracings showed alteration of auditory BER whereas tonal audiometry was normal. Analysis of BER demonstrated lengthening of the latency periods, a rise in thresholds without latency period increases and a tracing that was sometimes flat or with waves that were difficult to recognize.

[Auditory and vestibular lesions in Behcet's disease].

Auditory and vestibular function tests were conducted in 16 patients with Behcet's disease. Vestibular lesions included spontaneous nystagmus in 5 cases, and a bilateral vestibular syndrome after provoked tests in 13 cases (7 of the deficiency type and 6 irritative in nature). Findings after auditory tests were bilateral symmetric deafness in 2 cases; one of the perception type and the other showing mixed features.