[Kearns-Sayre syndrome: a case report].

Kearns-Sayre syndrome (KSS), first described in 1958, is a multisystem disease defined by a characteristic triad of progressive external ophthalmoplegia, pigmentary retinopathy and atrioventricular block. These signs are frequently associated with increased cerebrospinal fluid protein level and cerebellar ataxia. This syndrome is caused by deletions in mitochondrial DNA, the age of onset is generally below 20, and the degree of severity differs between patients, as well as the prognosis, which may be fatal.

[Exsudative retinal detachment indicative of a giant cell arteritis. A case report].

Giant cell arteritis (Horton's disease) is an inflammatory panarteritis occurring most frequently in the elderly. Its common ocular manifestations are anterior ischemic optic neuropathy, choroidal ischemia and central retinal artery occlusion. We describe a case of Horton's disease revealed by a retinal detachment, optic neuropathy and severe choroidal ischemia.

[Orbital apex syndrome secondary to herpes zoster infection. A case report].

The orbital apex syndrome is defined by the association of visual loss, ophtalmoplegia, blepharoptosis, proptosis along with forehead and upper eyelid anesthesia. This syndrome is secondary to traumatism, malignancy or infection of orbital apex. Herpes zoster is an uncommon cause.

[Bilateral Sturge-Weber-Krabbe syndrome. A case report].

Sturge-Weber-Krabbe syndrome is a rare congenital neuro-oculo-cutaneous disease, characterized by an unilateral facial vascular nevus which affects at least the first branch of the trigeminal nerve, associated with an ipsilateral leptomeningeal angioma and ipsilateral vascular lesions of the choroid sometimes leading to glaucoma. Variants of this classical presentation have been described in the literature, some of which have prognosis significance. We report an unusual case of an 11-year-old male with a serious bilateral glaucoma associated with a bilateral facial nevus flammeus and cerebral calcifications without neurological symptoms.

[Ophthalmomyiasis interna: two case studies].

Myiasis is a pathology caused by the presence of fly larvae in the human organism. Ophthalmomyiasis interna is characterized by the presence of the parasite within the eye but also in the eyelids and the orbit. Herein, the authors present the clinical cases of two patients presenting ophthalmomyiasis interna revealed by retinal detachment for the first patient and by panuveitis for the second patient.