Introduction: Spinal epidermoid cysts are noncancerous growths that comprise fewer than 1 % of the abnormalities found in the spine. An epidermoid cyst in the intradural extramedullary region, without any associated dysraphism, trauma, or syndromic conditions, and its subsequent successful identification and surgical removal without any adverse effects on the patient, is a highly uncommon event.
Case Presentation: A 2-year-old female visited the outpatient clinic with a skin fold on the back that has been present since birth, without any abnormalities in the spinal cord or any injuries.