Diagnosis and treatment of extraabdominal desmoid fibromatosis.

Introduction: The desmoid fibromatosis is a very rare connective tissue disease which is recognized as semimalignant. The aim of this work is to review the relevant literature and to analyze the management of our patient collective.

Material And Method: Surgery was performed on 7 patients with extraabdominal desmoid fibromatosis between August 1998 and May 2007.