Long-term non-invasive positive pressure ventilation among cystic fibrosis patients awaiting lung transplantation.

Background: Pulmonary disease is the most frequent cause of morbidity and mortality in cystc fibrosis patients. New techniques such as non-invasive positive pressure ventilation have resulted in prolongation of life expectancy in CF patients with end-stage lung disease.

Objectives: To determine the role of NIPPV in CF patients awaiting lung transplantation.