Appreciation of the treatment in adult patients with congenital portosystemic connections in relation with their symptoms.

Background: portosystemic intrahepatic venous connections (Abernethy syndrome) are rare anatomical variants, which are classified according to the type of union between the portal venous circulation and the central venous system. In adults, the diagnosis is often incidental, although some cases can be presented with an encephalopathy without associated liver disease.

Case Reports: here we present two cases of portosystemic shunt, one with encephalopathy development, and the other casually caught.