Publications by authors named "Agnes Brun"

Article Synopsis
  • Cilia are essential organelles linked to various genetic disorders called ciliopathies, which often result in retinal degeneration (RD).
  • This study compares retinal degeneration mechanisms in three rodent models representative of different ciliopathies: Bardet-Biedl Syndrome, Alström Syndrome, and CEP290-mediated Leber Congenital Amaurosis, using techniques like electroretinography and electron microscopy.
  • Findings show that BBS and CEP290 models share a similar rapid degeneration process with specific cellular dysfunctions, while the ALMS model exhibits a slower degeneration without certain defects, indicating that each ciliopathy has unique disease progression pathways despite all leading to vision loss.
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Herein we report, for the first time, an overall evaluation of commercially available battery separators to be used for aluminum batteries, revealing that most of them are not stable in the highly reactive 1-ethyl-3-methylimidazolium chloride:aluminum trichloride (EMIMCl:AlCl) electrolyte conventionally employed in rechargeable aluminum batteries. Subsequently, a novel highly stable polyacrylonitrile (PAN) separator obtained by the electrospinning technique for application in high-performance aluminum batteries has been prepared. The developed PAN separator has been fully characterized in terms of morphology, thermal stability, and air permeability, revealing its suitability as a separator for battery applications.

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