Superior oblique tendon (Brown's) syndrome as the presenting finding in childhood onset HLA-B27-related enthesitis and juvenile idiopathic oligoarticular arthritis.

We report two patients who presented with Brown's syndrome. The first is a 7-year-old boy who at the time of his diagnosis was also found to have enthesitis and HLA-B27 positivity. The second patient was diagnosed with bilateral Brown's syndrome at 13 months of age.

Comparison of inferior oblique myectomy to recession for the treatment of superior oblique palsy.

Purpose: To compare inferior oblique (IO) myectomy with recession for the treatment of superior oblique (SO) palsy.

Methods: A retrospective review of medical records identified all patients with SO palsy who underwent IO weakening procedures. Patients were excluded if IO muscle surgery was bilateral, combined with other vertical muscle surgery and if follow up was less than 4 weeks.

Retinoblastoma with autoinfarction presenting as orbital cellulitis.

We describe a case of unilateral retinoblastoma in a 13-month-old boy who presented with signs of orbital cellulitis. Heterochromia, hyphema, and vitreous hemorrhage were observed. Initial computed tomography (CT) imaging failed to reveal the calcified intraocular mass that was later identified on ultrasonography.

Oculodentodigital dysplasia: new ocular findings and a novel connexin 43 mutation.

Objectives: To describe new ocular findings associated with oculodentodigital dysplasia (ODDD) and a novel mutation in the connexin 43 transmembrane domain.

Design: Oculodentodigital dysplasia is a rare autosomal dominant disease characterized by multiple systemic abnormalities, most commonly of the ocular, nasal, dental, and limb structures. Herein, we studied 2 patients with ODDD.

Descemet stripping automated endothelial keratoplasty in a 2-year-old child.

Endothelial transplantation in the form of Descemet stripping endothelial keratoplasty (DSEK) or Descemet stripping automated endothelial keratoplasty (DSAEK) has rapidly become a popular, if not the preferred, method of treating endothelial failure. Although the need to perform corneal transplantation in children with endothelial dysfunction is relatively rare, this situation does arise, and in children still in the amblyogenic age group, rapid recovery from an essentially refractive-neutral corneal procedure carries significant advantages. We describe the use of DSAEK in a 2-year-old child who exhibited irreversible corneal edema from endothelial damage secondary to complicated cataract surgery.