[5-year results of arterial correction in transposition of great vessels].

A prospective study was performed on in-hospital patients between June 1985 and July 1992 to assess the 5 year results of surgical detransposition of the great arteries. Clinical examination, electrocardiography, echocardiography, right and left heart catheterisation with selective coronary angiography, isotopic right and left ventricular ejection fractions at rest and with infusion of dobutamine and SestaMibi myocardial perfusion scintigraphy at rest and with dipyridamole, were performed during the 5th year after surgery. Twenty-six children underwent this protocol: eight others did not come for examination because they had moved from the region, one of whom had suffered regressive postoperative myocardial infarction.

[Familial supravalvular aortic stenosis. Investigation in a family and review of the literature].

Familial supravalvular aortic stenosis is a rare autosomal dominant condition. It may be distinguished from the Williams-Beuren syndrome by the absence of the characteristic dysmorphic appearances and of mental retardation. The case of a 9-year-old girl with a severe surgical stenosis led to the diagnosis of the same malformation in the mother and two brothers.

[Tilt-table test. Value in children and adolescents].

The tilt test is a non-invasive investigation which reproduces malaises or vagal syncope. This is a common condition in children and adolescents and the value of this investigation in this population is therefore self-evident. The tilt test was performed from 4 years of age in 105 children aged 4 to 18 years (mean 10 +/- 4 years) who had suffered one or several malaises with syncope.

[Diagnosis using x-ray computed angiotomography of an iliac artery aneurysm in an infant].

The authors describe an infant with an aneurysm of the right iliac artery, associated with three sites involving the inferior mesenteric artery and its first two branches, most likely related to an episode of chicken pox. Helical angiography with computed tomography, performed with a continuous-rotation scanner, allowed precise assessment of the lesions, in particular those affecting the inferior mesenteric artery.

[Anomalous origin of the left main coronary artery from the right coronary sinus and trajectory to the great vessels. Value of echocardiography in a child].

During a routine medical check-up, a pathological electrocardiogram was recorded in an asymptomatic 6 year old girl. The demonstration of coronary insufficiency by exercise stress testing and sestamib myocardio-scintigraphy led to the diagnosis of an anomalous origin of the left coronary artery. This vessel arose from the right coronary sinus and continued anteriorly to the main coronary artery.