Monorchidism or unilateral anorchidism.

Unilateral anorchidism, or monorchidism, refers to the absence of one testis. It is defined as the unilateral or bilateral partial or complete absence of testicular tissue, with or without rudimentary epididymal and spermatic cord remnants, in the presence of internal Wolffian duct development and normal external genitalia. In the case of monorchidism with derivatives of the Wolffian duct an ipsilateral testis must be present at least up to the 16th week of gestation to induce the formation of an epididymal structure.

Anomalies of the position of the spleen in the child. Case report and review of the literature from 1896 to 1990.

We report on the case of a 6-year-old girl admitted as an emergency with an acute abdomen with the diagnosis of peritonitis; clinical examination under anesthesia revealed the presence of an abdomino-pelvic mass. Laparotomy confirmed the diagnosis of torsion of an ectopic spleen. Splenectomy was required because the spleen was gangrenous.

[Accidents in children and adolescents].

Injury is the most important threat to health of children and the leading cause of death in children after the first year of life. The death of an otherwise normal child is a tragedy. Crippling injuries to a child and the need for rehabilitation have a greater effect on our health system; the child's image of himself as an incomplete individual is another tragedy during the whole life of a child.

[The blue rubber bleb nevus or the cellular blue nevus or Bean syndrome. A rare case of iron-deficiency anemia].

Described by Bean in 1958 the Blue rubber bleb nevus syndrome is a viscero-cutaneous hemangiomatosis, a rare condition associating typical cutaneous and visceral hemangiomas of the cavernous type. We report the case of a four year old boy who presented a microcytic and hyperchromic anemia. The previous medical history of this boy was characterized by a large cavernous angioma on the right hand operated on the at the age of three months.

[Unilateral anorchidism or monorchidism].

Monorchidism is a Testicular Regression Syndrome (Vanishing Testis Syndrome), defined as the unilateral or bilateral partial and complete absence of testicular tissue with or without rudimentary epididymal and spermatic cord remnants in the presence of normal duct development and normal external genitalia. In this paper we report the results of a personal series of 36 patients. We discuss the histopathology and try to answer the question whether protection of the solitary contralateral testis by orchidopexy is necessary in monorchidism.